Wednesday, October 17, 2012

Dyke Davidoff Masson Syndrome

Dyke Davidoff Masson Syndrome (DDMS) is a neurodegenerative disorder likely due to cerebral injury in utero or early in life. The main finding is cerebral hemiatrophy. Associated findings include ipsilateral compensatory calvarial thickening, enlarged frontal sinus, elevation of the petrous ridge and sphenoid wing.

The above images are from a young boy who presented with a history of seizures. There is asymmetric atrophy of the left cerebral hemisphere. Bone window examination demonstrates enlargement of the left frontal sinus.

Grossman RI, Yousem DM. Neuroradiology, the requisites. Mosby Inc. (2003)

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