Association of Intraductal Papillary Mucinous Tumor with Autosomal Dominant Polycystic Kidney Disease

There are scattered case reports of autosomal dominant polycystic kidney disease (ADPKD) and polycystic liver disease in association with intraductal papillary mucinous tumors (IPMTs). On the other hand, a cystic pancreatic lesion in a patient ADPKD could be a simple pancreatic cyst, which is seen in up to 10% of patients with ADPKD.

References

• Sato Y, Mukai M, Sasaki M, Kitao A, Yoneda N, Kobayashi D, Imamura Y, Nakanuma Y. Intraductal papillary-mucinous neoplasm of the pancreas associated with polycystic liver and kidney disease. Pathol Int. 2009 Mar;59(3):201-4.
• Naitoh H, Shoji H, Ishikawa I, Watanabe R, Furuta Y, Tomozawa S, Igarashi H, Shinozaki S, Katsura H, Onozato R, Kudoh M. Intraductal papillary mucinous tumor of the pancreas associated with autosomal dominant polycystic kidney disease. J Gastrointest Surg. 2005 Jul-Aug;9(6):843-5.