Midaortic Dysplastic Syndrome

Midaortic dysplastic syndrome refers to hypertension and weakness or absence of the femoral pulses due to diffuse narrowing of the mid thoracoabdominal aorta. There is often involvement of renal and mesenteric arteries.

Midaorticdysplastic syndrome may have an identical appearance to late-phase type II Takayasu arteritis. The two can be differentiated by biopsy by noting inflammatory change in patients with Takayasu arteritis but not in midaortic dysplastic syndrome.

Collateral parietal arteries connect the thoracic aorta and the abdominal aorta, most commonlyfrom the subclavian artery to the internal mammary artery to the superior epigastric artery to the inferior epigastric artery to the external iliac artery.

  Patients may be treated with aortic reconstruction using prosthetic or autologous venous grafts.

References

Sebastià C, Quiroga S, Boyé R, Perez-Lafuente M, Castellà E, Alvarez-Castells A. Aortic stenosis: spectrum of diseases depicted at multisection CT. Radiographics. 2003 Oct;23 Spec No:S79-91