Gorlin Syndrome

Gorlin Syndrome, also known as basal cell nevus syndrome, is characterized by multiple odontogenic keratocysts (OKC), prominent dural calcifications, and macrocephaly. Other findings include, hyperaerated paranasal sinuses, rib anomalies (splayed, fused, or bifid), kyphosis, platybasia, and Sprengel deformity of the scapula.

The image shows dural calcifications (blue arrow), at least one odontogenic keratocyst (pink arrow), a bifid left second rib (green arrow), and a Sprengel deformity of the left scapula (yellow arrow).